Amyotrophic lateral sclerosis - ALS: progression of the disease in diagnosed patients

Authors

DOI:

https://doi.org/10.5281/zenodo.7199354

Keywords:

Esclerose Lateral Amiotrófica, Progressão da Esclerose Lateral Amiotrófica, Enfermagem na Esclerose Lateral Amiotrófica, Terapêutica na ELA, Fatores de risco ELA, Diagnóstico da Esclerose Lateral Amiotrófica

Abstract

Objective: Dissert about the progression of Amyotrophic Lateral Sclerosis - ALS in diagnosed patients and discourse about the nurse's role in ALS’s therapy. Methods: The study is about a bibliographic integrative revision, between 2017-2022, through research in the electronic data base of the Scientific Electronic Library Online (Scielo), PubMed, BVS and Lilacs. Results: Twenty-six articles were used in this article, the relation between the content of the article and the theme determined in this article was crucial for the elaboration during the dissertation, by showing the most important information and the conclusion of several authors, divided in six categories: The development of the disease; Risk factors; Diagnosis; Symptomatology and its complications; Therapy; and the nurse’s role in ALS. Conclusion: The study allowed purchase knowledge about the disease, although it is still in constant discovery. The treatment of the pathology occurs through palliative care, planning the interventions according to the patient’s condition, with the objective to provide quality of life for the patient, the patient’s family members and the patients' caregivers. The Riluzol was the most effective medication in the treatment of ALS, increasing the survival and assuaging the symptoms. Beyond that, some risk factors for the development of the disease were pointed out. About the nurse’s role in ALS, it was set that their role is very important during the progression of the disease's course and the pathology’s treatment of the diagnosed patient with ALS.

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Author Biographies

Ana Beatriz Rangel Diniz, Universidade Paulista, UNIP, Brasil

Graduanda em Enfermagem pela Universidade Paulista.

mceclip0.png https://orcid.org/0000-0003-3519-1217
mceclip1.png http://lattes.cnpq.br/6236559612248331
Universidade Paulista, UNIP, Brasil
E-mail: anabeatrd123@gmail.com

Marco Aurélio Ninômia Passos, Universidade Paulista, UNIP, Brasil

Graduado em Ciências Biológicas pela Universidade Católica de Brasília. Mestre em Ciências Genômicas e Biotecnologia pela Universidade Católica de Brasília. Doutor em Biologia Molecular pela Universidade de Brasília.

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Published

2022-10-14

How to Cite

DINIZ, A. B. R.; PASSOS, M. A. N. Amyotrophic lateral sclerosis - ALS: progression of the disease in diagnosed patients. JRG Journal of Academic Studies, Brasil, São Paulo, v. 5, n. 11, p. 160–180, 2022. DOI: 10.5281/zenodo.7199354. Disponível em: http://www.revistajrg.com/index.php/jrg/article/view/404. Acesso em: 12 may. 2024.

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